The core is formed by an outer shell (pericardium), a muscular layer (myocardium) and an inner wrapper (endocardium). Restrictive cardiomyopathy is a rare heart disease in which there is a thickening of the myocardium preventing the heart to enlarge and fill properly.
The myocardium is the muscle of the heart to perform its function of pump. In restrictive cardiomyopathy, the heart becomes so rigid that you can not relax properly during diastole, during the time in which is dilated and the blood returns to the heart filling. In more advanced stages may be affected also function contraction (systole) and pump blood.
The cause of this disease may be unknown (often occurs after a heart transplant), or due to diseases that cause the heart muscle to thicken as amyloidosis, hemochromatosis and sarcoidosis, some tumor infiltration or radiation fibrosis .
The inability for adequate filling of the heart generates a series of symptoms resulting from a pumping less blood appearing dyspnea or shortness of breath, fatigue, and fluid accumulation in the legs (edema), abdomen (ascites) and enlargement of the liver.
Diagnosis is based on physical examination and medical signs and abnormal cardiac auscultation and distended neck veins. Furthermore, based on a series of tests:
Treatment is usually ineffective and is mainly focused on improving heart function deteriorated and its consequences and the quality of life of patients.
Is advised salt restriction diet and drugs that facilitate the function of the heart and removing fluids (diuretics).
It also indicates the specific treatment of the underlying disease that is causing cardiomyopathy in cases possible.
In certain circumstances and corticosteroids may be used if cardiac function is severely damaged heart transplantation can be considered.
There are no known measures to prevent this disease.
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